A man in New York developed an extremely rare and fatal brain disorder after he ate squirrel brains, according to a new report of the man's case.

In 2015, the 61-year-old man was brought to a hospital in Rochester, New York, after experiencing a decline in his thinking abilities and losing touch with reality, the report said. The man had also lost the ability to walk on his own.

An MRI of the man's head revealed a striking finding: The brain scan looked similar to those seen in people with variant Creutzfeldt-Jakob disease (vCJD), a fatal brain condition caused by infectious proteins called prions.

....the man had another dietary habit that could have raised his risk for vCJD: His family said he liked to hunt, and it was reported that he had eaten squirrel brains, said Dr. Tara Chen, a medical resident at Rochester Regional Health and lead author of the report. It's unclear if the man consumed the entire squirrel brain or just squirrel meat that was contaminated with parts of squirrel brain,

Usually no brains left after I shoot them

Maybe a crazy eyeball

Moral of the story: don't eat brains!

Old timers around home would eat them with eggs. I never took part.

The same thing was noted in Kentucky back in the '90s. A whole bunch of people acquired a "mad squirrel disease". Back then they were reporting it as a variant of mad cow. Like Creutzfeldt-Jakob, it's a prion disease. All of the affected people were squirrel brain-eaters. All of them died.

Same thing can happen from eating all sorts of brain, including human brains (Kuru disease).

Moral of the story: don't eat brains!

A man who ate squirrel brains may have died after catching rare mad cow-like disease

By Scott Berson

[email protected]


October 17, 2018 10:58 AM

Updated October 17, 2018 07:36 PM

A new report says a Rochester, NY., hunter may have developed an ultra-rare brain infection after eating the brains of squirrels he killed, according LiveScience.

The report was presented at the ID (infectious disease) week conference as an abstract called “Towards Earlier Diagnosis of Transmissible Spongiform Encephalopathies (TSEs): A Case Series, Including One Associated with Squirrel Brain Consumption.”

The report identified a 61-year-old male who was diagnosed with the rare brain infection called variant Creutzfeldt-Jakob Disease after eating squirrel brains. He arrived at a hospital after suffering thinking problems and an impaired walk, according to the report. He died about five months after being diagnosed with the infection in 2015.

The disease is similar to “mad cow disease,” which causes tiny holes to fill the brain until the tissue looks like a sponge (which is where ‘”spongiform” comes from), according to the National Institutes of Health.
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The infection is always fatal, and most who get the disease live around a year. It causes rapid degeneration of memory, thinking, vision and coordination before causing dementia and death, according to the NIH.

It is part of a family of diseases caused by prions, which are infectious proteins that infiltrate the brain. Chronic wasting disease in deer is one example of a prion disease, as is fatal familial insomnia, a different brain infection affecting humans that removes the ability to sleep, eventually causing death.

Variant Creutzfeldt-Jakob disease is extremely rare, with only four people ever confirmed to have the disease in the U.S., according to the Centers for Disease Control.

The non-variant Creutzfeldt-Jakob Disease is also rare, with only about 350 cases per year in the United States, according to the NIH. Most people develop the disease spontaneously, while a few inherit it. Some acquire it through other means, such as by ingesting infected tissue - which is what scientists suspect happened with the squirrel brains.

The USDA announced there is a cow that was tested positive for mad cow disease. Officials do say they pose no health risks.
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Tara Chen, a medical student who produced the report, said it wasn’t entirely clear yet if the squirrel brains were the cause of the infection, and that researchers were trying to secure autopsy samples, according to LiveScience. Chen said it also wasn’t clear if the man ate the brains themselves or meat that was contaminated with brain matter, according to the site.

Squirrel-brain transmission of the disease is not a new concern. Doctors in Kentucky put out a warning against eating squirrel brains in 1997 after 11 people were diagnosed in the state with the non-variant Creutzfeldt-Jakob Disease, according to the New York Times.

“‘All of them were squirrel-brain eaters,’‘ a doctor told the paper at the time.


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Researchers say a New York man may have been infected with Creutzfeldt-Jakob Disease after eating squirrel brains from hunting. The disease is similar to mad cow disease and leads to dementia and death. Robert F. Bukaty AP